CME Klippel-Trenaunay Syndrome
نویسندگان
چکیده
Learning Objectives: After studying this article, the participant should be able to: 1. Define the triad of signs and symptoms that describe Klippel-Trenaunay syndrome. 2. Speculate on the various theories regarding its pathogenesis. 3. Discuss the necessary radiologic workup required to pursue appropriate management. 4. Restate the most common reasons for surgically treating this syndrome. 5. Formulate a concise and appropriate management protocol for patients with Klippel-Trenaunay syndrome.
منابع مشابه
Klippel-Trenaunay syndrome and malignant Melanoma: Coincidence or association (A case report)
A 37-year-old woman with Klippel-Trenaunay syndrome who developed malignant melanoma on the limb affected the vascular malformation, is reported. The observation and nature of this association or coincidence is discussed.
متن کاملReport of a case of Klippel-Trenaunay syndrome associated with bilateral nevus of Ota
Port-wine stain is a vascular malformation characterized pathologically by ectasia of superficial dermal capillaris and clinically by persistent macular erythema. The association of a port-wine stain on a limb with soft tissue swelling, with or without bony overgrowth, is termed klippel-Trenaunay syndrome. Phakomatosis pigmento-vascularis is a combination of port-wine stain and cutaneous ...
متن کاملKlippel - Trenaunay - Weber syndrome — a case report
syndrome is a rare congenital syndrome involving enlarged veins and arteries, limb hypertrophy and capillary malformations. In 1900, French physicians, Klippel and Trenaunay, first described what became known as Klippel-Trenaunay syndrome after two patients presented with a triad of symptoms — port-wine stain, varicose veins, and bony and soft tissue hypertrophy involving an extremity (Klippel ...
متن کاملKlippel–Trenaunay–Weber syndrome with atypical presentation of hypersplenism and nephrotic syndrome: a case report
BACKGROUND Klippel-Trenaunay-Weber syndrome is a rare syndrome; unfortunately, very few studies of the connection between hypersplenism, nephrotic syndrome, and Klippel-Trenaunay-Weber syndrome have been published. CASE PRESENTATION We report the case of a 40-year-old white man with a typical clinical presentation of Klippel-Trenaunay-Weber syndrome, including "port-wine stains," varicose vei...
متن کاملKlippel-Trenaunay Syndrome with Extensive Lymphangiomas
Klippel-Trenaunay syndrome (KTS) is a rare disorder characterized by the triad of vascular malformations, venous varicosities, and bone and soft-tissue hypertrophy. We present a case of Klippel-Trenaunay syndrome with limb hypertrophy, port-wine stains, lymphangiomas, and venous varicosities in the limbs.
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تاریخ انتشار 2002